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Abstract
RÉSUMÉ
Le double arc aortique associé à une atrésie pulmonaire à septum ouvert(APSO) est une anomalie congénitale rare. Nous rapportons le cas d’un nourrisson de 1 mois qui présente un double arc aortique associé à une APSO. Il s’agissait d’un nourrisson d’un mois, de sexe féminin, admis pour un bilan cardiologique après un épisode de détresse respiratoire. Dans ses antécédents, nous retrouvions une infection néonatale. Il était cyanosé sans souffle cardiaque. L’électrocardiogramme inscrivait un axe hypergauche et une hypertrophie ventriculaire droite. L’échocardiographie avait conclu à une APSO. L’angioscanner réalisé dans le cadre du bilan préopératoire avait conclu à une APSO associée à un double arc aortique avec un arc gauche qui se termine en cul-de-sac par un canal artériel qui alimente l’artère pulmonaire gauche. Il était décédé avant la chirurgie dans un tableau de détresse respiratoire. Ce cas illustre que le DAA peut être associé à une APSO. L’angioscanner est l’élément central du diagnostic. Le traitement est chirurgical.
ABSTRACT
Double aortic arch associated with pulmonary atresia with ventricular septal defect is a rare congenital anomaly. We report a case of a 1-month-old infant with Double aortic arch associated with pulmonary atresia with ventricular septal defect. This was a one-month-old female infant admitted for cardiological workup after an episode of respiratory distress. His history included a neonatal infection. He was cyanotic with no heart murmur. The electrocardiogram showed a hyperleft axis and right ventricular hypertrophy. The echocardiography concluded to be an pulmonary atresia with ventricular septal defect. The angioscanner performed as part of the preoperative work-up showed an pulmonary atresia with ventricular septal defect associated with a double aortic arch with a left arch that terminates with a ductus arteriosus that feeds the left pulmonary artery. He died before surgery in respiratory distress. This case illustrates that the double aortic arch can be associated with an pulmonary atresia with ventricular septal defect. Angioscan is central to the diagnosis. Treatment is surgical.
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References
- Liang Y, Zhou Q, Chen Z. Double aortic arch with ascending aortic aneurysm and aortic valve regurgitation. Ann Thorac Surg. 2014;97(2):e43–e45.
- Gross RE. Arterial malformations which cause compression of the trachea or esophagus. Circulation. 1955;11(1):124–134
- Sihame Lemouakni, Amale Hassani, Hakim Elyajouri, Mohammed Kmari, Hakim Ourrai, Rachid Abilkacem, et Aomar Agadr. Double arc aortique: à propos de deux cas). Pan Afr Med J. 2017; 27: 273. DOI : 10.11604/pamj.2017.27.273.13481)
- Han Seok Seo, Yong Hyun Park, Ju Hyoung Lee, So Chong Hur, Yu Jin Ko, So Yeon Park et al. Case of Balanced Type Double Aortic Arch Diagnosed Incidentally by Transthoracic Echocardiography in an Asymptomatic Adult Patient.J Cardiovasc Ultrasound. 2011 Sep;19(3):163-166
- Backer CL, Mavroudis C, Rigsby CK, Holinger LD. Trends in vascular ring surgery. J Thorac Cardiovasc Surg. 2005;129(6):1339–1347
- Lee ML. Diagnosis of the double aortic arch and its differentiation from the conotruncal malformations. Yonsei Med J 2007;48:818–826.
- van Son JA, Julsrud PR, Hagler DJ, Sim EK, Puga FJ, Schaff HV, Danielson GK. Imaging strategies for vascular rings. Ann Thorac Surg 1994;57:604–610
- Lillehei CW, Colan S. Echocardiography in the preoperative evaluation of vascular rings. J Pediatr Surg 1992;27:1118–1120
- Kellenberger CJ. Aortic arch malformations. Pediatr Radiol 2010;40:876–884
- Mark Ruzmetov⁎, Palaniswamy Vijay, Mark D. Rodefeld, Mark W. Turrentine, John W. Brown . Follow-up of surgical correction of aortic arch anomalies causing tracheoesophageal compression: a 38-year single institution experience. Journal of Pediatric Surgery (2009) 44, 1328–1332
- Fernando Cesar Gimenes Barbosa Santos; Ulisses Alexandre Croti; Carlos Henrique De Marchi; Sírio Hassem Sobrinho. Double Aortic Arch Associated with Pulmonary Atresia with Ventricular Septal Defect. Braz J Cardiovasc Surg 2016;31(1):63-5
References
Liang Y, Zhou Q, Chen Z. Double aortic arch with ascending aortic aneurysm and aortic valve regurgitation. Ann Thorac Surg. 2014;97(2):e43–e45.
Gross RE. Arterial malformations which cause compression of the trachea or esophagus. Circulation. 1955;11(1):124–134
Sihame Lemouakni, Amale Hassani, Hakim Elyajouri, Mohammed Kmari, Hakim Ourrai, Rachid Abilkacem, et Aomar Agadr. Double arc aortique: à propos de deux cas). Pan Afr Med J. 2017; 27: 273. DOI : 10.11604/pamj.2017.27.273.13481)
Han Seok Seo, Yong Hyun Park, Ju Hyoung Lee, So Chong Hur, Yu Jin Ko, So Yeon Park et al. Case of Balanced Type Double Aortic Arch Diagnosed Incidentally by Transthoracic Echocardiography in an Asymptomatic Adult Patient.J Cardiovasc Ultrasound. 2011 Sep;19(3):163-166
Backer CL, Mavroudis C, Rigsby CK, Holinger LD. Trends in vascular ring surgery. J Thorac Cardiovasc Surg. 2005;129(6):1339–1347
Lee ML. Diagnosis of the double aortic arch and its differentiation from the conotruncal malformations. Yonsei Med J 2007;48:818–826.
van Son JA, Julsrud PR, Hagler DJ, Sim EK, Puga FJ, Schaff HV, Danielson GK. Imaging strategies for vascular rings. Ann Thorac Surg 1994;57:604–610
Lillehei CW, Colan S. Echocardiography in the preoperative evaluation of vascular rings. J Pediatr Surg 1992;27:1118–1120
Kellenberger CJ. Aortic arch malformations. Pediatr Radiol 2010;40:876–884
Mark Ruzmetov⁎, Palaniswamy Vijay, Mark D. Rodefeld, Mark W. Turrentine, John W. Brown . Follow-up of surgical correction of aortic arch anomalies causing tracheoesophageal compression: a 38-year single institution experience. Journal of Pediatric Surgery (2009) 44, 1328–1332
Fernando Cesar Gimenes Barbosa Santos; Ulisses Alexandre Croti; Carlos Henrique De Marchi; Sírio Hassem Sobrinho. Double Aortic Arch Associated with Pulmonary Atresia with Ventricular Septal Defect. Braz J Cardiovasc Surg 2016;31(1):63-5