Tumeur Germinale Sécrétante de la Glande Pinéale de l’Enfant : à Propos d’un Cas

Angèle H Pondy Ongotsoyi, Hubert Désiré Mbassi Awa, Francisca Monebenimp, Paul Koki Ndombo

Abstract


RÉSUMÉ
L’incidence des tumeurs cérébrales chez l’enfant est faible dans les pays pauvres par rapport aux pays industrialisés, probablement parce qu’un grand nombre d’enfants décèdent sans diagnostic précis du fait des ressources financières limitées d’une part et de l’absence d’accès aux techniques modernes de diagnostic d’autres part. Nous rapportons l’observation d’un garçon de 12 ans portant un drain ventriculopéritonéal placé en urgence devant une hypertension intracrânienne tumorale. La localisation pinéale et les caractères de la tumeur en IRM avaient fait suspecter une tumeur germinale. L’élévation de l’alphafœtoprotéine a confirmé le diagnostic de tumeur germinale sécrétante de la glande pinéale. La chimiothérapie a fait disparaître tous les symptômes.
ABSTRACT
The incidence of pediatric cerebral tumors is low in developing countries compared to industrialized countries; probably because many children die prior to diagnosis either because of limited financial resources or because of the limited access to modern technologies of diagnosis. We report the case of a 12 year old boy with an emergency placement of ventriculoperitoneal shunt because of tumoral intracranial hypertension. Pineal localization and MRI features lead to the diagnosis of a germinal tumor. The elevation of the alpha fetoprotein tumoral marker confirmed the diagnosis of secreting germ cell tumor of the pineal region. Chemotherapy alleviated all the symptoms.


Keywords


Tumeur germinale cérébrale - Marqueurs tumoraux - Chimiothérapie

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