La Sclérocornée Congénitale Bilatérale: À Propos d’un Cas

Stève Robert Ebana Mvogo, D Enyama, AV Dohvoma, C Ebana Mvogo

Abstract


La sclérocornée congénitale appartient au groupe des opacifications cornéennes congénitales. En plus du problème esthétique que cette pathologie pose, le pronostic visuel est en général sombre. L’ultra biomicroscopie doit être systématique pour compléter le diagnostic et classifier l’anomalie. Le conseil génétique est nécessaire et l’indication d’une greffe de cornée se discute en fonction du bilan lésionnel et du pronostic. Nous rapportons un cas de sclérocornée congénitale bilatérale chez un nourrisson de 2 mois afin d’attirer l’attention des praticiens sur cette pathologie rare et difficile à prendre en charge dans notre contexte.

ABSTRACT
Congenital clouding of the cornea can be caused by congenital sclerocornea amongst other causes. This condition is associated with poor visual prognosis besides the aesthetic problem. In order to complete the diagnosis and classify the condition, ultrasound biomicroscopy is the gold standard. Corneal transplantation can solve the problem with a proper indication. Genetic counselling should be systematic. The treatment of this disease is difficult in our country. We report a case of congenital bilateral sclerocornea in a 2 months old infant with the aim of drawing the attention of medical practitioners to this rare condition and underlining the difficulties in managing such patients in our setting.


Keywords


Sclérocornée, ultra biomicroscopie, conseil génétique, greffe de cornée.

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